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Title: Recommendations for the management of autoinflammatory diseases.
Author: Ter Haar, Nienke M.
Oswald, Marlen
Jeyaratnam, Jerold
Antón López, Jordi
Barron, Karyl
Brogan, Paul
Cantarini, Luca
Galeotti, Caroline
Grateau, Gilles
Hentgen, Veronique
Hofer, Michael
Kallinich, Tilmann
Koné-Paut, Isabelle
Lachmann, Helen J.
Ozdogan, Huri
Ozen, Seza
Russo, Ricardo
Simon, Anna
Uziel, Yosef
Wouters, Carine
Feldman, Brian
Vastert, Sebastiaan J.
Wulffraat, Nico
Benseler, Susanne M.
Frenkel, Joost
Gattorno, Marco
Kuemmerle-Deschner, Jasmin
Keywords: Inflamació
Salut pública
Public health
Issue Date: 24-Jun-2015
Publisher: BMJ Publishing Group
Abstract: Autoinflammatory diseases are characterised by fever and systemic inflammation, with potentially serious complications. Owing to the rarity of these diseases, evidence-based guidelines are lacking. In 2012, the European project Single Hub and Access point for paediatric Rheumatology in Europe (SHARE) was launched to optimise and disseminate regimens for the management of children and young adults with rheumatic diseases, facilitating the clinical practice of paediatricians and (paediatric) rheumatologists. One of the aims of SHARE was to provide evidence-based recommendations for the management of the autoinflammatory diseases cryopyrin-associated periodic syndromes (CAPS), tumour necrosis factor (TNF) receptor-associated periodic syndrome (TRAPS) and mevalonate kinase deficiency (MKD). These recommendations were developed using the European League Against Rheumatism standard operating procedure. An expert committee of paediatric and adult rheumatologists was convened. Recommendations derived from the systematic literature review were evaluated by an online survey and subsequently discussed at a consensus meeting using Nominal Group Technique. Recommendations were accepted if more than 80% agreement was reached. In total, four overarching principles, 20 recommendations on therapy and 14 recommendations on monitoring were accepted with ≥ 80% agreement among the experts. Topics included (but were not limited to) validated disease activity scores, therapy and items to assess in monitoring of a patient. By developing these recommendations, we aim to optimise the management of patients with CAPS, TRAPS and MKD.
Note: Reproducció del document publicat a:
It is part of: Annals of the Rheumatic Diseases, 2015, vol. 74, num. 9, p. 1636-1644
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ISSN: 0003-4967
Appears in Collections:Articles publicats en revistes (Cirurgia i Especialitats Medicoquirúrgiques)

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