Browsing by Subject Malalties neuromusculars

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Issue DateTitleAuthor(s)
16-Apr-2015Androgen receptor aggregates studies in vitro and in a transgenic mouse model of Spinal Bulbal Muscular Atrophpy (SMBA)Eftekharzadeh, Bahareh
11-May-2012Aplicación de técnicas de proteómica para el estudio de enfermedades neuromuscularesTorre Gómez, Carolina de la
30-Jul-2003L'Atròfia Muscular Espinal durant el desenvolupament humà. Mecanismes de mort cel·lular i expressió de gens i proteïnes involucrades en la malaltiaSoler Botija, Carolina
1-Feb-2021Brain iron deficiency changes the stoichiometry of adenosine receptor subtypes in cortico-striatal terminals. Implications for restless legs syndromeRodrigues, Matilde S.; Ferreira, Samira G.; Quiroz, César; Earley, Christopher J.; García Borreguero, Diego; Cunha, Rodrigo A.; Ciruela Alférez, Francisco; Köfalvi, Attila; Ferré, Sergi
4-Sep-2024Cannabidiol ameliorates mitochondrial disease via PPARγ activation in preclinical modelsPuighermanal, Emma; Luna-Sánchez, Marta; Gella, Alejandro; van der Walt, Gunter; Urpi, Andrea; Royo, María; Tena-Morraja, Paula; Appiah, Isabella; de Donato, Maria Helena; Menardy, Fabien; Bianchi, Patrizia; Esteve-Codina, Anna; Rodríguez-Pascau, Laura; Vergara Paños, Cristina; Gómez-Pallarès, Mercè; Marsicano, Giovanni; Bellocchio, Luigi; Martinell, Marc; Sanz, Elisenda; Jurado, Sandra; Soriano Zaragoza, Francesc X. (Francesc Xavier); Pizcueta Lalanza, María Pilar; Quintana, Albert
11-Dec-2018Challenges and future prospects on 3D in-vitro modeling of the neuromuscular circuitBadiola Mateos, Maider; Hervera Abad, Arnau; Río Fernández, José Antonio del; Samitier i Martí, Josep
10-Mar-2021Compartmentalised microfluidic culture systems for in vitro modelling of neurological and neuromuscular microenvironmentsBadiola Mateos, Maider
Jun-2020Consistent improvement with eculizumab across muscle groups in myasthenia gravisMantegazza, Renato; O'Brien, Fanny L.; Yountz, Marcus; Howard, James F. Jr.; REGAIN Study Group; Casasnovas Pons, Carlos
16-Dec-2024Deciphering the importance of heterogeneity in Myotonic Dystrophy type 1Núñez Manchón, Judit
23-Nov-2012Desarrollo neuromuscular en la atrofia muscular espinalMartínez Hernàndez, Rebeca
2021Discovery of a Potent Dual Inhibitor of Acetylcholinesterase and Butyrylcholinesterase with Antioxidant Activity that Alleviates Alzheimer-like Pathology in Old APP/PS1 MiceViayna, Elisabet; Coquelle, Nicolas; Cieslikiewicz-Bouet, Monika; Cisternas, Pedro; Oliva, Carolina; Sánchez-López, E. (Elena); Ettcheto Arriola, Miren; Bartolini, Manuela; De Simone, Angela; Ricchini, Mattia; Rendina, Marisa; Pons, Mégane; Firuzi, Omidreza; Pérez, Belén; Saso, Luciano; Andrisano, Vincenza; Nachon, Florian; Brazzolotto, Xavier; García, Maria Luisa; Camins Espuny, Antoni; Silman, Israel; Jean, Ludovic; Inestrosa, Nibaldo C.; Colletier, Jacques-Philippe; Renard, Pierre-Yves; Muñoz-Torrero López-Ibarra, Diego
13-Jan-2016Early and gender-specific differences in spinal cord mitochondrial function and oxidative stress markers in a mouse model of ALSCacabelos, Daniel; Ramírez Núñez, Omar; Granado Serrano, Ana Belén; Torres, Pascual; Ayala, Victòria; Moiseeva, Victoria; Povedano, Mònica; Ferrer, Isidro (Ferrer Abizanda); Pamplona, Reinald; Portero-Otin, Manuel; Boada, Jordi
1-Jun-2020Eculizumab as a promising treatment in thymoma-associated myasthenia gravisVélez Santamaria, Valentina; Nedkova Hristova, Velina; Díez, Laura; Homedes, Christian; Alberti, Maria Antonia; Casasnovas Pons, Carlos
1982Enfermedad neuromuscular oculocraniosomática de Kearns Sayre: a propósito de tres casosRamió Masgrau, Rosa Maria; Codina Puiggrós, Agustí; Navarro, Carmen; Ferrer, Isidro (Ferrer Abizanda); Barceló, A.; Fito, A.; Boada, Mercè; Dávalos, Antoni; Matias-Guiu, Xavier, 1958-
18-Mar-2021Estimation of the prevalence and incidence of motor neuron diseases in two Spanish regions: Catalonia and ValenciaBarceló Rado, Ma. Antonia (María Antonia); Povedano, Mònica; Vázquez Costa, Juan F.; Franquet, Álvaro; Solans, Marta; Saez, Marc
29-Nov-2024Identificación de predictores de arritmias cardíacas y muerte súbita en pacientes pediátricos afectos de enfermedades neuromuscularesCésar Diaz, Sergio
11-Mar-2018Increasing polarity in tacrine and huprine derivatives: Potent anticholinesterase agents for the treatment of myasthenia gravisGaldeano Cantador, Carlos; Coquelle, Nicolas; Cieslikiewicz-Bouet, Monika; Bartolini, Manuela; Pérez, Belén; Clos, Victòria; Silman, Israel; Jean, Ludovic; Colletier, Jacques-Philippe; Renard, Pierre-Yves; Muñoz-Torrero López-Ibarra, Diego
27-Sep-2019Motor neuron diseases caused by a novel VRK1 variant – A genotype/phenotype studySedghi, Maryam; Moslemi, Ali‐Reza; Olivé i Plana, Montserrat; Etemadifar, Masoud; Ansari, Behnaz; Nasiri, Jafar; Emrahi, Leila; Mianesaz, Hamid‐Reza; Laing, Nigel G.; Tajsharghi, Homa
4-Nov-2020Myasthenia gravis exacerbation after melatonin administration: case series from a tertiary referral centreNedkova Hristova, Velina; Vélez Santamaria, Valentina; Casasnovas Pons, Carlos
24-Dec-2022Myasthenia Gravis Induced by Immune Checkpoint Inhibitors: An Emerging Neurotoxicity in Neuro-Oncology Practice: Case SeriesMarco, Carla; Simó, Marta; Alemany, Montse; Casasnovas, Carlos; Domínguez, Raúl; Vilariño, Noelia; Calvo, Mariona; Martín Liberal, Juan; Brenes, Jesús; Sabater Riera, Joan; Bruna, Jordi; Velasco, Roser