Browsing by Subject Prion diseases

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Issue DateTitleAuthor(s)
30-Aug-2012A common BACE1 polymorphism is a risk factor for sporadic Creutzfeldt-Jakob diseaseCalero, Olga; Bullido, María Jesús; Clarimón, Jordi; Frank García, Ana; Martínez Martín, Pablo; Lleó Bisa, Alberto; Rey, María Jesús; Sastre, Isabel; Rábano, Alberto; Pedro Cuesta, Jesús de; Ferrer, Isidro (Ferrer Abizanda); Calero, Miguel
27-Jul-2018Altered gene transcription linked to astrocytes and oligodendrocytes in frontal cortex in Creutzfeldt-Jakob diseaseAndrés Benito, Pol; Domínguez González, Mayelín; Ferrer, Isidro (Ferrer Abizanda)
2010APP processing and b-amyloid deposition in sporadic Creutzfeldt-Jakob patients is dependent on Dab1.Gavín Marín, Rosalina; Ferrer, Isidro (Ferrer Abizanda); Río Fernández, José Antonio del
2-May-2020Assessment of glial activation response in the progress of natural scrapie after chronic dexamethasone treatmentGuijarro, Isabel M.; Garcés Crespo, Miguel; Andrés Benito, Pol; Marín, Belén; Otero, Alicia; Barrio Castro, Tomás del; Carmona Murillo, Margarita; Ferrer, Isidro (Ferrer Abizanda); Badiola, Juan J.; Monzón, Marta
1-May-2020BAMBI and CHGA in Prion Diseases: Neuropathological Assessment and Potential Role as Disease BiomarkersLópez Pérez, Óscar; Bernal Martín, Marcos; Hernaiz, Adelaida; Llorens Torres, Franc; Betancor, Marina; Otero, Alicia; Toivonen, Janne Markus; Zaragoza, Pilar; Zerr, Inga; Badiola, Juan José; Bolea, Rosa; Martín Burriel, Inmaculada
20-May-2003Biodiagnóstico de las enfermedades por priones humanasSánchez del Valle Díaz, Raquel
1-Feb-2019Cerebrospinal fluid neurofilament light in suspected sporadic Creutzfeldt-Jakob diseaseKanata, Eirini; Golanska, Ewa; Villar Piqué, Anna; Karsanidou, Aikaterini; Dafou, Dimitra; Xanthopoulos, Konstantinos; Schmitz, Matthias; Ferrer, Isidro (Ferrer Abizanda); Karch, André; Sikorska, Beata; Liberski, Pawel P.; Sklaviadis, Theodoros; Zerr, Inga; Llorens Torres, Franc
Jun-2018Cerebrospinal fluid neurofilament light levels in neurodegenerative dementia: Evaluation of diagnostic accuracy in the differential diagnosis of prion diseasesZerr, Inga; Schmitz, Matthias; Karch, André; Villar Piqué, Anna; Kanata, Eirini; Golanska, Ewa; Diaz-Lucena, Daniela; Llorens Torres, Franc; Hermann, Peter; Knipper, Tobias; Goebel, Stefan; Varges, Daniela; Sklaviadis, Theodoros; Sikorska, Beata; Liberski, Pawel P.; Ladogana, Anna; Ferrer, Isidro (Ferrer Abizanda); Zetterberg, Henrik; Blennow, Kaj; Calero, Miguel; Sánchez del Valle Díaz, Raquel; Baldeiras, Inês
1-Jan-2020Cerebrospinal fluid neurogranin as a new player in prion disease diagnosis and prognosisVillar Piqué, Anna; Llorens, Franc; Zerr, Inga
1-Apr-2019Cerebrospinal fluid total prion protein in the spectrum of prion diseasesVillar Piqué, Anna; Schmitz, Matthias; Lachmann, Ingolf; Karch, André; Calero, Olga; Stehmann, Christ; Sarros, Shannon; Ladogana, Anna; Poleggi, Anna; Santana, Isabel; Ferrer, Isidro (Ferrer Abizanda); Mitrova, Eva; Žáková, Dana; Pocchiari, Maurizio; Baldeiras, Inês; Calero, Miguel; Collins, Steven J.; Geschwind, Michael D.; Sánchez del Valle Díaz, Raquel; Zerr, Inga; Llorens Torres, Franc
11-Oct-2012Coexistence of protease sensitive and resistant prion protein in 129VV homozygous sporadic Creutzfeldt-Jakob disease: a case reportRodríguez Martínez, Ana B.; López de Munain, Adolfo; Ferrer, Isidro (Ferrer Abizanda); Zarranz, Juan J.; Atarés, Begoña; Villagra, Nuria T.; Arteagoitia, José María; Garrido, Joseba M.; Juste, Ramón A.
1-Jan-2021Differential astrocyte and oligodendrocyte vulnerability in murine Creutzfeldt-Jakob diseaseAndrés Benito, Pol; Carmona Murillo, Margarita; Douet, Jean Yves; Cassard, Hervé; Andreoletti, Olivier; Ferrer, Isidro (Ferrer Abizanda)
15-Nov-2017Differential overexpression of SERPINA3 in human prion diseasesVanni, Silvia; Moda, Fabio; Zattoni, Marco; Bistaffa, E.; Cecco, E. De; Rossi, Marcello; Giaccone, Giorgio; Tagliavini, Fabrizio; Haik, Stéphane; Deslys, Jean-Philippe; Zanusso, Gianluigi; Ironside, James W.; Ferrer, Isidro (Ferrer Abizanda); Kovacs, Gabor G.; Legname, Giuseppe
19-Nov-2012Establiment de metodologia analítica per a la purificació, separació i caracterització de biomarcadors proteics de malalties neurodegenerativesBorges Álvarez, Marta
29-Mar-2007Estudi de l'excreció i estabilitat de prions en el mediMaluquer de Motes i Porta, Carles
16-Mar-2018Funciones de la proteína priónica celular, alfa-sinucleína y reelina en enfermedades neurodegenerativasUrrea Zazurca, Laura
2017Hereditary Human Prion Diseases: an UpdateSchmitz, Matthias; Dittmar, Kathrin; Llorens Torres, Franc; Gelpi, Ellen; Ferrer, Isidro (Ferrer Abizanda); Schulz-Schaeffer, Walter J.; Zerr, Inga
9-Sep-2021Histotype-Dependent Oligodendroglial PrP Pathology in Sporadic CJD: A Frequent Feature of the M2C “Strain”Gelpi, Ellen; Klotz, Sigrid; Vidal Robau, Nuria; Ricken, Gerda; Regelsberger, Günther; Ströbel, Thomas; Kalev, Ognian; Leoni, Marlene; Budka, Herbert; Kovacs, Gabor G.
30-Jun-2022Innovative Non-PrP-Targeted Drug Strategy Designed to Enhance Prion ClearanceColini Baldeschi, Arianna; Zattoni, Marco; Vanni, Silvia; Nikolic, Lea; Ferracin, Chiara; La Sala, Giuseppina; Summa, Maria; Bertorelli, Rosalia; Bertozzi, Sine Mandrup; Giachin, Gabriele; Carloni, Paolo; Bolognesi, Maria Laura; De Vivo, Marco; Legname, Giuseppe
2010Involvement of Dab1 in APP processing and [beta]-amyloid deposition in sporadic Creutzfeldt-Jakob patients.Gavín Marín, Rosalina; Ferrer, Isidro (Ferrer Abizanda); Río Fernández, José Antonio del