Browsing by Subject Prions

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Issue DateTitleAuthor(s)
25-Oct-2010A novel form of human disease with a protease-sensitive prion protein and heterozygosity methionine/valine at codon 129: Case reportRodríguez Martínez, Ana B.; Garrido, Joseba M.; Zarranz, Juan J.; Arteagoitia, José María; Pancorbo, Marian M. de; Atarés, Begoña; Bilbao, Miren J.; Ferrer, Isidro (Ferrer Abizanda); Juste, Ramón A.
27-Apr-2017Altered Ca2+ homeostasis induces Calpain-Cathepsin axis activation in sporadic Creutzfeldt-Jakob diseaseLlorens Torres, Franc; Thüne, Katrin; Sikorska, Beata; Schmitz, Matthias; Tahir, Waqas; Fernández Borges, Natalia; Cramm, Maria; Gotzmann, Nadine; Carmona Murillo, Margarita; Streichenberger, Nathalie; Michel, Uwe; Zafar, Saima; Schuetz, Anna-Lena; Rajput, Ashish; Andreoletti, Olivier; Bonn, Stefan; Fischer, Andre; Liberski, Pawel P.; Torres, Juan Maria; Ferrer, Isidro (Ferrer Abizanda); Zerr, Inga
23-Oct-2019Development of a New largely scalable in vitro prion propagation method for the production of infectious recombinant prions for high resolution structural studies.Eraña, Hasier; Charco, Jorge M.; Di Bari, Michele A.; Díaz Domínguez, Carlos M.; López Moreno, Rafael; Vidal, Enric; González Miranda, Ezequiel; Pérez Castro, Miguel A.; García Martínez, Sandra; Bravo, Susana; Fernández Borges, Natalia; Geijo, Mariví; Agostino, Claudia D'; Garrido, Joseba; Bian, Jifeng; König, Anna; Uluca Yazgi, Boran; Sabaté Lagunas, Raimon; Khaychuk, Vadim; Vanni, Ilaria; Telling, Glenn C.; Heise, Henrike; Nonno, Romolo; Requena, Jesús R.; Castilla, Joaquín
12-Feb-2020Diagnostic accuracy of prion disease biomarkers in iatrogenic Creutzfeldt-Jakob diseaseLlorens Torres, Franc; Villar Piqué, Anna; Hermann, Peter; Schmitz, Matthias; Calero, Olga; Stehmann, Christiane; Sarros, Shannon; Moda, Fabio; Ferrer, Isidro (Ferrer Abizanda); Poleggi, Anna; Pocchiari, Maurizio; Catania, Marcella; Klotz, Sigrid; O'Regan, Carl; Brett, Francesca; Heffernan, Josephine; Ladogana, Anna; Collins, Steven J.; Calero, Miguel; Kovacs, Gabor G.; Zerr, Inga
7-Aug-2018Discovering Putative Prion-Like Proteins in Plasmodium falciparum: A Computational and Experimental AnalysisPallarès, Irantzu; Groot, Natalia S. de; Iglesias, Valentín; Sant'Anna, Ricardo; Biosca, Arnau; Fernàndez Busquets, Xavier; Ventura, Salvador
16-Mar-2018Funciones de la proteína priónica celular, alfa-sinucleína y reelina en enfermedades neurodegenerativasUrrea Zazurca, Laura
22-Jan-2018Hemoglobin mRNA Changes In The Frontal Cortex Of Patients With Neurodegenerative DiseasesVanni, Silvia; Zattoni, Marco; Moda, Fabio; Giaccone, Giorgio; Tagliavini, Fabrizio; Haik, Stéphane; Deslys, Jean-Philippe; Zanusso, Gianluigi; Ironside, James W.; Carmona Murillo, Margarita; Ferrer, Isidro (Ferrer Abizanda); Kovacs, Gabor G.; Legname, Giuseppe
30-Jun-2022Innovative Non-PrP-Targeted Drug Strategy Designed to Enhance Prion ClearanceColini Baldeschi, Arianna; Zattoni, Marco; Vanni, Silvia; Nikolic, Lea; Ferracin, Chiara; La Sala, Giuseppina; Summa, Maria; Bertorelli, Rosalia; Bertozzi, Sine Mandrup; Giachin, Gabriele; Carloni, Paolo; Bolognesi, Maria Laura; De Vivo, Marco; Legname, Giuseppe
1-Mar-2018Involvement of Cellular Prion Protein in alpha-Synuclein Transport in NeuronsUrrea Zazurca, Laura; Segura Feliu, Miriam; Masuda-Suzukake, Masami; Hervera Abad, Arnau; Pedraz López, Lucas; García Aznar, José Manuel; Vila, Miquel; Samitier i Martí, Josep; Torrents Serra, Eduard; Ferrer, Isidro (Ferrer Abizanda); Gavín Marín, Rosalina; Hagesawa, Masato; Río Fernández, José Antonio del
2010Involvement of Dab1 in APP processing and [beta]-amyloid deposition in sporadic Creutzfeldt-Jakob patients.Gavín Marín, Rosalina; Ferrer, Isidro (Ferrer Abizanda); Río Fernández, José Antonio del
1-Apr-2018iPS cell cultures from a Gerstmann-Straussler-Scheinker patient with the Y218N PRNP mutation recapitulate tau pathologyMatamoros i Anglès, Andreu; Mayela Gayosso, Lucia; Richaud-Patin, Yvonne; Domenico, Angelique Di; Vergara Paños, Cristina; Hervera Abad, Arnau; Sousa, Amaia; Fernández Borges, Natalia; Consiglio, Antonella; Gavín Marín, Rosalina; López de Maturana, Rakel; Ferrer, Isidro (Ferrer Abizanda); López de Munain, Adolfo; Raya Chamorro, Ángel; Castilla, Joaquín; Sanchez-Pernaute, Rosario; Río Fernández, José Antonio del
22-Apr-2016Key Points for the Amyloid Infectivity and Prion Neuronal InvasionEspargaró Colomé, Alba; Busquets i Viñas, Ma. Antonia; Estelrich i Latràs, Joan; Sabaté Lagunas, Raimon
29-Nov-2013La proteína priónica celular: Análisis de su función neuroprotectora y reguladora del ciclo CelularCarulla Martí, Patricia
1-Dec-2021MED15 prion-like domain forms a coiled-coil responsible for its amyloid conversion and propagationBatlle, Cristina; Calvo Serrano, Isabel; Iglesias, Valentin; Lynch, Cian J.; Gil García, Marcos; Serrano Marugán, Manuel; Ventura, Salvador
29-Jun-2011Neuroprotective role of PrPC against kainate-induced epileptic seizures and cell death depends on the modulation of JNK3 activation by GluR6/7-PSD-95 bindingCarulla Martí, Patricia; Bribián Arruego, Ana; Rangel Rincones, Alejandra Helena; Gavín Marín, Rosalina; Ferrer, Isidro (Ferrer Abizanda); Caelles Franch, Carme; Río Fernández, José Antonio del; Llorens Torres, Franc
5-Aug-2013Neurotoxicity of prion peptides mimicking the central domain of the cellular prion proteinVilches Saez, Silvia; Vergara Paños, Cristina; Nicolás i Pallejà, Josep Oriol; Sanclimens Pérez de Rozas, Glòria; Varón, S.; Acosta, Gerardo A.; Albericio Palomera, Fernando; Royo Expósito, Miriam; Río Fernández, José Antonio del; Gavín Marín, Rosalina
2009New insights into cellular prion protein (PrPc) functions: the 'ying and yang' of a relevant protein.Nicolás i Pallejà, Josep Oriol; Gavín Marín, Rosalina; Río Fernández, José Antonio del
25-Apr-2019Noves funcions de PrP(c) en neurotransmissió, neuroprotecció i neurodegeneracióMatamoros i Anglès, Andreu
19-Feb-2020On the Binding of Congo Red to Amyloid FibrilsEspargaró Colomé, Alba; Llabrés Prat, Salomé; Saupe, Sven J.; Curutchet Barat, Carles E.; Luque Garriga, F. Xavier; Sabaté Lagunas, Raimon
19-Nov-2020Optimization of the Real-Time Quaking-Induced Conversion Assay for Prion Disease DiagnosisZerr, Inga; Cramm, Maria; Silva Correia, Susana Margarida da; Zafar, Saima; Villar Piqué, Anna; Llorens Torres, Franc; Schmitz, Matthias