Carregant...
Miniatura

Tipus de document

Article

Versió

Versió publicada

Data de publicació

Llicència de publicació

cc-by (c) Badiola Mateos, Maider et al., 2018
Si us plau utilitzeu sempre aquest identificador per citar o enllaçar aquest document: https://hdl.handle.net/2445/138717

Challenges and future prospects on 3D in-vitro modeling of the neuromuscular circuit

Títol de la revista

Director/Tutor

ISSN de la revista

Títol del volum

Resum

Movement of skeletal-muscle fibers is generated by the coordinated action of several cells taking part within the locomotion circuit (motoneurons, sensory-neurons, Schwann cells, astrocytes, microglia, and muscle-cells). Failure s in any part of this circuit could impede or hinder coordinated muscle movement and cause a neu romuscular disease (NMD) or determine its severity. Studying fragments of the circuit cannot provide a comprehensive and complete view of the pathological process. We trace the historic developments of studies focused on in-vitro modeling of the spinal-locomotion circuit and how bioengineered innovative technologies show advantages for an accurate mimicking of hysiological conditions of spinal-locomotion circuit. New developments on compartmentalized microfluidic culture systems (cμFCS), the use of human induced pluripotent stem cells (hiPSCs) and 3D cell-cultures are analyzed. We finally address limitations of current study models and three main challenges on neuromuscular studies: (i) mimic the whole spinal-locomotion circuit including all cell-types involved and the evaluation of independent and interdependent roles of each one; (ii) mimic the neurodegenerative response of mature neurons in-vitro as it occurs in-vivo ; and (iii) develop, tune, implement, and combine cμFCS, hiPSC, and 3D-culture technologies to ultimately create patient-specific complete, translational, and reliable NMD in-vitro model. Overcoming these challenges would significantly facilitate understanding the events taking place in NMDs and accelerate the process of finding new therapies.

Citació

Citació

BADIOLA MATEOS, Maider, HERVERA ABAD, Arnau, RÍO FERNÁNDEZ, José antonio del, SAMITIER I MARTÍ, Josep. Challenges and future prospects on 3D in-vitro modeling of the neuromuscular circuit. _Frontiers in Bioengineering and Biotechnology_. 2018. Vol. 6, núm. 194. [consulta: 26 de febrer de 2026]. ISSN: 2296-4185. [Disponible a: https://hdl.handle.net/2445/138717]

Exportar metadades

JSON - METS

Compartir registre