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cc by-nc-nd (c) Riera Mestre, Antoni et al, 2024
Si us plau utilitzeu sempre aquest identificador per citar o enllaçar aquest document: https://hdl.handle.net/2445/214867

Preguntas PICO y metodología DELPHI para mejorar el manejo de los pacientes con porfiria hepática aguda

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Background: Acute hepatic porphyrias (AHPs) are a group of rare diseases that encompasses acute intermittent porphyria, variegate porphyria, hereditary coproporphyria, and 5-aminolaevulinic acid dehydratase deficiency porphyria. Symptoms of AHP are nonspecific which, together with its low prevalence, difficult the diagnosis and follow-up of these patients. Material and methods: This project used DELPHI methodology to answer PICO questions related to management of patients with AHPs. The objective was to reach a consensus among multidisciplinary porhyria experts providing answers to those PICO questions for improving diagnosis and follow-up of patients with AHP. Results: Ten PICO questions were defined and grouped in four domains: 1. Biochemical diagnosis of patients with AHP. 2. Molecular tests for patients with AHP. 3. Follow-up of patients with AHP. 4. Screening for long-term complications of patients with AHP. Conclusions: PICO questions and DELPHI methodology have provided a consensus on relevant and controversial issues for improving the management of patients with AHP.

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RIERA MESTRE, Antoni, et al. Preguntas PICO y metodología DELPHI para mejorar el manejo de los pacientes con porfiria hepática aguda. Revista Clínica Española. 2024. Vol. 224, num. 5, pags. 272-280. ISSN 1578-1860. [consulted: 24 of May of 2026]. Available at: https://hdl.handle.net/2445/214867

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